{"id":11119,"date":"2025-08-27T22:29:43","date_gmt":"2025-08-27T19:29:43","guid":{"rendered":"https:\/\/dryavuzbesogul.com\/ebstein-anomalisi-nedir\/"},"modified":"2025-08-28T20:55:37","modified_gmt":"2025-08-28T17:55:37","slug":"ebstein-anomalisi-nedir","status":"publish","type":"post","link":"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/","title":{"rendered":"Ebstein Anomalisi Nedir? Belirtileri ve Tedavisi"},"content":{"rendered":"<p>Ebstein anomalisi, trik\u00fcspit kapa\u011f\u0131n do\u011fu\u015ftan yap\u0131sal bozuklu\u011fu ile karakterize nadir bir kalp hastal\u0131\u011f\u0131d\u0131r. Bu durumda trik\u00fcspit kapak yaprak\u00e7\u0131klar\u0131 normalden a\u015fa\u011f\u0131da, sa\u011f kar\u0131nc\u0131\u011fa do\u011fru yerle\u015fmi\u015ftir ve kapak tam olarak kapanamaz.<\/p>\n<p>Kapa\u011f\u0131n anormal konumu nedeniyle sa\u011f kulak\u00e7\u0131k geni\u015fler, sa\u011f kar\u0131nc\u0131k k\u00fc\u00e7\u00fcl\u00fcr ve kan\u0131n geriye ka\u00e7\u0131\u015f\u0131 (trik\u00fcspit yetmezli\u011fi) olu\u015fur. Bu durum, kalbin pompalama verimini d\u00fc\u015f\u00fcr\u00fcr ve zamanla sa\u011f kalp yetmezli\u011fine yol a\u00e7abilir.<\/p>\n<p>Belirtiler hafif formda yok denecek kadar az olabilirken, ileri vakalarda morarma, nefes darl\u0131\u011f\u0131, \u00e7arp\u0131nt\u0131, yorgunluk ve bacaklarda \u015fi\u015flik g\u00f6r\u00fclebilir. Baz\u0131 hastalarda ritim bozukluklar\u0131 da geli\u015febilir.<\/p>\n<p>Tan\u0131, ekokardiyografi ile konur; ileri inceleme olarak manyetik rezonans g\u00f6r\u00fcnt\u00fcleme veya kateterizasyon gerekebilir. Tedavi, hastal\u0131\u011f\u0131n \u015fiddetine g\u00f6re ila\u00e7 tedavisi, ritim d\u00fczenleyici giri\u015fimler veya trik\u00fcspit kapak onar\u0131m\u0131\/de\u011fi\u015fimini i\u00e7erebilir.<\/p>\n<table>\n<tbody>\n<tr>\n<td>Tan\u0131m<\/td>\n<td>Trik\u00fcspit kapak\u00e7\u0131\u011f\u0131n do\u011fu\u015ftan anormal yerle\u015fimi ve yap\u0131sal bozuklu\u011fu nedeniyle sa\u011f kalp odac\u0131klar\u0131n\u0131n etkilenmesiyle karakterize do\u011fumsal bir kalp hastal\u0131\u011f\u0131<\/td>\n<\/tr>\n<tr>\n<td>Nedenler<\/td>\n<td>Do\u011fu\u015ftan geli\u015fimsel bozukluk; genellikle nedeni kesin bilinmez, nadiren genetik veya \u00e7evresel fakt\u00f6rler<\/td>\n<\/tr>\n<tr>\n<td>Risk Fakt\u00f6rleri<\/td>\n<td>Do\u011fu\u015ftan kalp hastal\u0131\u011f\u0131 \u00f6yk\u00fcs\u00fc, annenin gebelik s\u0131ras\u0131nda lityum kullan\u0131m\u0131, genetik yatk\u0131nl\u0131k<\/td>\n<\/tr>\n<tr>\n<td>Belirtiler<\/td>\n<td>Morarma (siyanoz), nefes darl\u0131\u011f\u0131, \u00e7arp\u0131nt\u0131, yorgunluk, \u00e7abuk yorulma, b\u00fcy\u00fcme-geli\u015fme gerili\u011fi, aritmi, bay\u0131lma<\/td>\n<\/tr>\n<tr>\n<td>Tan\u0131 Y\u00f6ntemleri<\/td>\n<td>Ekokardiyografi (en \u00f6nemli tan\u0131 y\u00f6ntemi), EKG, akci\u011fer grafisi, kardiyak MR, kardiyak kateterizasyon<\/td>\n<\/tr>\n<tr>\n<td>Tedavi Y\u00f6ntemleri<\/td>\n<td>Takip (hafif olgularda), ila\u00e7 tedavisi (kalp yetmezli\u011fi ve aritmi i\u00e7in), cerrahi (trik\u00fcspit kapak tamiri veya de\u011fi\u015fimi), ileri vakalarda kalp nakli<\/td>\n<\/tr>\n<tr>\n<td>Komplikasyonlar<\/td>\n<td>Kalp yetmezli\u011fi, ciddi ritim bozukluklar\u0131, ani kalp durmas\u0131, b\u00fcy\u00fcme-geli\u015fme gerili\u011fi, emboli<\/td>\n<\/tr>\n<tr>\n<td>\u00d6nleme Y\u00f6ntemleri<\/td>\n<td>Spesifik \u00f6nleme yoktur; riskli gebelerde ila\u00e7 kullan\u0131m\u0131na dikkat, do\u011fumsal kalp hastal\u0131klar\u0131nda erken tan\u0131 ve takip<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\n\t<section class=\"section\" id=\"section_82707756\">\n\t\t<div class=\"section-bg fill\" >\n\t\t\t\t\t\t\t\t\t\n\t\t\t\n\n\t\t<\/div>\n\n\t\t\n\n\t\t<div class=\"section-content relative\">\n\t\t\t\r\n\r\n<div class=\"row\"  id=\"row-1905680896\">\r\n\r\n\n\t<div id=\"col-2024033513\" class=\"col small-12 large-12\"  >\n\t\t\t\t<div class=\"col-inner\" style=\"background-color:#02288a;\" >\n\t\t\t\n\t\t\t\r\n\r\n<div class=\"row\"  id=\"row-2047465140\">\r\n\r\n\n\t<div id=\"col-467534643\" class=\"col medium-4 small-12 large-4\"  >\n\t\t\t\t<div class=\"col-inner\"  >\n\t\t\t\n\t\t\t\r\n\r\n\t<div class=\"img has-hover border-gorsel x md-x lg-x y md-y lg-y\" id=\"image_481923760\">\n\t\t\t\t\t\t\t\t<div class=\"img-inner dark\" >\n\t\t\t<img decoding=\"async\" width=\"700\" height=\"700\" src=\"https:\/\/dryavuzbesogul.com\/wp-content\/uploads\/2025\/08\/yavuz-besogul-banner.jpg\" class=\"attachment-2048x2048 size-2048x2048\" alt=\"\" srcset=\"https:\/\/dryavuzbesogul.com\/wp-content\/uploads\/2025\/08\/yavuz-besogul-banner.jpg 700w, https:\/\/dryavuzbesogul.com\/wp-content\/uploads\/2025\/08\/yavuz-besogul-banner-400x400.jpg 400w, https:\/\/dryavuzbesogul.com\/wp-content\/uploads\/2025\/08\/yavuz-besogul-banner-280x280.jpg 280w\" sizes=\"(max-width: 700px) 100vw, 700px\">\t\t\t\t\t\t\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\n<style>\n#image_481923760 {\n  width: 100%;\n}\n<\/style>\n\t<\/div>\n\t\r\n\r\n\r\n\t\t<\/div>\n\t\t\t\t\n<style>\n#col-467534643 > .col-inner {\n  border-radius: 20px;\n}\n<\/style>\n\t<\/div>\n\n\t\r\n\n\t<div id=\"col-209923739\" class=\"col medium-8 small-12 large-8\"  >\n\t\t\t\t<div class=\"col-inner dark\"  >\n\t\t\t\n\t\t\t\r\n\r\n<p><strong><span style=\"font-size: 150%;\">Prof. Dr. Yavuz Be\u015fo\u011ful<\/span><\/strong><\/p>\r\n<p>>Turkey\u2019s Cardiovascular Surgery Doctor<\/p>\r\n<div>\r\n<div>Professor Doctor Yavuz Be\u015fo\u011ful is one of the first doctors to perform heart surgeries with minimally invasive methods in cardiovascular surgery since 1997. In Turkey, he published his first patient series on subaxillary (armpit) surgeries in 1999, 2001, 2002, 2003, and 2004 in national and international scientific congresses and journals, and these were accepted in international and national congresses.<\/div>\r\n<\/div>\r\n<div><\/div>\r\n\t<div id=\"gap-1171010291\" class=\"gap-element clearfix\" style=\"display:block; height:auto;\">\n\t\t\n<style>\n#gap-1171010291 {\n  padding-top: 30px;\n}\n<\/style>\n\t<\/div>\n\t\r\n\r\n<a href=\"https:\/\/dryavuzbesogul.com\/en\/prof-dr-yavuz-besogul\/\" class=\"button white lowercase hide-for-small\"  style=\"border-radius:15px;\">\n\t\t<span>About<\/span>\n\t<\/a>\n\r\n\r\n<a href=\"https:\/\/dryavuzbesogul.com\/en\/iletisim\/\" class=\"button white lowercase hide-for-small\"  style=\"border-radius:15px;\">\n\t\t<span>Contact<\/span>\n\t<\/a>\n\r\n\r\n<div class=\"row show-for-small\"  id=\"row-152390731\">\r\n\r\n\n\t<div id=\"col-792922184\" class=\"col medium-6 small-6 large-6\"  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30px;\n}\n<\/style>\n\t<\/section>\n\t\n<div id=\"ez-toc-container\" class=\"ez-toc-v2_0_82_2 counter-hierarchy ez-toc-counter ez-toc-custom ez-toc-container-direction\">\n<div class=\"ez-toc-title-container\">\n<p class=\"ez-toc-title\" style=\"cursor:inherit\">Yaz\u0131 \u0130\u00e7eri\u011fi<\/p>\n<span class=\"ez-toc-title-toggle\"><a href=\"#\" class=\"ez-toc-pull-right ez-toc-btn ez-toc-btn-xs ez-toc-btn-default ez-toc-toggle\" aria-label=\"Toggle Table of Content\"><span class=\"ez-toc-js-icon-con\"><span class=\"\"><span class=\"eztoc-hide\" style=\"display:none;\">Toggle<\/span><span class=\"ez-toc-icon-toggle-span\"><svg style=\"fill: #ffffff;color:#ffffff\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" class=\"list-377408\" width=\"20px\" height=\"20px\" viewBox=\"0 0 24 24\" fill=\"none\"><path d=\"M6 6H4v2h2V6zm14 0H8v2h12V6zM4 11h2v2H4v-2zm16 0H8v2h12v-2zM4 16h2v2H4v-2zm16 0H8v2h12v-2z\" fill=\"currentColor\"><\/path><\/svg><svg style=\"fill: #ffffff;color:#ffffff\" class=\"arrow-unsorted-368013\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"10px\" height=\"10px\" viewBox=\"0 0 24 24\" version=\"1.2\" baseProfile=\"tiny\"><path d=\"M18.2 9.3l-6.2-6.3-6.2 6.3c-.2.2-.3.4-.3.7s.1.5.3.7c.2.2.4.3.7.3h11c.3 0 .5-.1.7-.3.2-.2.3-.5.3-.7s-.1-.5-.3-.7zM5.8 14.7l6.2 6.3 6.2-6.3c.2-.2.3-.5.3-.7s-.1-.5-.3-.7c-.2-.2-.4-.3-.7-.3h-11c-.3 0-.5.1-.7.3-.2.2-.3.5-.3.7s.1.5.3.7z\"\/><\/svg><\/span><\/span><\/span><\/a><\/span><\/div>\n<nav><ul class='ez-toc-list ez-toc-list-level-1 ' ><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-1\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_Anomalisi_Nedir\" >Ebstein Anomalisi Nedir?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-2\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_kalbi_nasil_etkiler\" >Ebstein anomalisi\u00a0 kalbi nas\u0131l etkiler?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-3\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_ile_birlikte_baska_kalp_sorunlari_gorulur_mu\" >Ebstein anomalisi ile birlikte ba\u015fka kalp sorunlar\u0131 g\u00f6r\u00fcl\u00fcr m\u00fc?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-4\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_neden_olur_ve_endiselenmeli_miyim\" >Ebstein anomalisi neden olur ve endi\u015felenmeli miyim?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-5\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_ne_gibi_belirtilere_yol_acar\" >Ebstein anomalisi ne gibi belirtilere yol a\u00e7ar?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-6\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_tanisi_icin_hangi_testler_yapilir\" >Ebstein anomalisi tan\u0131s\u0131 i\u00e7in hangi testler yap\u0131l\u0131r?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-7\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_hangi_ciddi_sorunlara_komplikasyonlara_yol_acabilir\" >Ebstein anomalisi hangi ciddi sorunlara (komplikasyonlara) yol a\u00e7abilir?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-8\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_icin_ameliyatsiz_tedavi_secenekleri_var_midir\" >Ebstein anomalisi i\u00e7in ameliyats\u0131z tedavi se\u00e7enekleri var m\u0131d\u0131r?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-9\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_ameliyati_ne_zaman_ve_kimler_icin_gereklidir\" >Ebstein anomalisi ameliyat\u0131 ne zaman ve kimler i\u00e7in gereklidir?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-10\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_cerrahisinde_hangi_ameliyat_yontemleri_uygulanir\" >Ebstein anomalisi cerrahisinde hangi ameliyat y\u00f6ntemleri uygulan\u0131r?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-11\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_ameliyati_sonrasi_surec_ve_uzun_donem_takip_nasil_isler\" >Ebstein anomalisi ameliyat\u0131 sonras\u0131 s\u00fcre\u00e7 ve uzun d\u00f6nem takip nas\u0131l i\u015fler?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-12\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_ile_saglikli_bir_yasam_surmek_mumkun_mu\" >Ebstein anomalisi ile sa\u011fl\u0131kl\u0131 bir ya\u015fam s\u00fcrmek m\u00fcmk\u00fcn m\u00fc?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-2'><a class=\"ez-toc-link ez-toc-heading-13\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Sikca_Sorulan_Sorular\" >S\u0131k\u00e7a Sorulan Sorular<\/a><ul class='ez-toc-list-level-3' ><li class='ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-14\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_nedir\" >Ebstein anomalisi nedir?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-15\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Bu_hastalik_ne_zaman_ortaya_cikar\" >Bu hastal\u0131k ne zaman ortaya \u00e7\u0131kar?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-16\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_belirtileri_nelerdir\" >Ebstein anomalisi belirtileri nelerdir?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-17\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Hangi_kapak_etkilenir\" >Hangi kapak etkilenir?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-18\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Bu_hastalik_neden_olur\" >Bu hastal\u0131k neden olur?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-19\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Nasil_teshis_edilir\" >Nas\u0131l te\u015fhis edilir?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-20\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Ebstein_anomalisi_her_zaman_belirti_verir_mi\" >Ebstein anomalisi her zaman belirti verir mi?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-21\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Hastaligin_ciddiyeti_kisiden_kisiye_degisir_mi\" >Hastal\u0131\u011f\u0131n ciddiyeti ki\u015fiden ki\u015fiye de\u011fi\u015fir mi?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-22\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Cerrahi_tedavi_gerekir_mi\" >Cerrahi tedavi gerekir mi?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-23\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Kateterle_tedavi_mumkun_mu\" >Kateterle tedavi m\u00fcmk\u00fcn m\u00fc?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-24\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Bu_hastalik_kalp_ritmini_etkiler_mi\" >Bu hastal\u0131k kalp ritmini etkiler mi?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-25\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Hamilelikte_Ebstein_anomalisi_riskli_midir\" >Hamilelikte Ebstein anomalisi riskli midir?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-26\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Yasam_beklentisi_nasildir\" >Ya\u015fam beklentisi nas\u0131ld\u0131r?<\/a><\/li><li class='ez-toc-page-1 ez-toc-heading-level-3'><a class=\"ez-toc-link ez-toc-heading-27\" href=\"https:\/\/dryavuzbesogul.com\/en\/ebstein-anomalisi-nedir\/#Egzersiz_yapilabilir_mi\" >Egzersiz yap\u0131labilir mi?<\/a><\/li><\/ul><\/li><\/ul><\/nav><\/div>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_Anomalisi_Nedir\"><\/span>Ebstein Anomalisi Nedir?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Ebstein anomalisi, kalpte trik\u00fcspit kapa\u011f\u0131n yap\u0131sal bozuklu\u011fuyla karakterize do\u011fu\u015ftan bir kalp hastal\u0131\u011f\u0131d\u0131r. Bu durumda trik\u00fcspit kapak normalden a\u015fa\u011f\u0131da yerle\u015fir ve sa\u011f kulak\u00e7\u0131k ile sa\u011f kar\u0131nc\u0131k aras\u0131ndaki s\u0131n\u0131r bozulur. Sonu\u00e7 olarak sa\u011f kulak\u00e7\u0131k b\u00fcy\u00fcr, sa\u011f kar\u0131nc\u0131\u011f\u0131n pompalama g\u00fcc\u00fc azal\u0131r ve kan dola\u015f\u0131m\u0131 bozulur. Belirtiler aras\u0131nda morarma, \u00e7arp\u0131nt\u0131, nefes darl\u0131\u011f\u0131, yorgunluk ve ritim bozukluklar\u0131 bulunur. Tedavi hastal\u0131\u011f\u0131n \u015fiddetine g\u00f6re ila\u00e7, kateter y\u00f6ntemleri veya cerrahi giri\u015fimle yap\u0131labilir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_kalbi_nasil_etkiler\"><\/span>Ebstein anomalisi\u00a0 kalbi nas\u0131l etkiler?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<div>\n<dl id=\"attachment_8562\">\n<dt><img decoding=\"async\" src=\"https:\/\/dryavuzbesogul.com\/wp-content\/uploads\/2020\/07\/Ebsteinin-anomali-diyagrami.jpg\" alt=\"Ebstein Anomalisi diyagram\u0131\" width=\"640\" height=\"371\" \/><\/dt>\n<dd>Ebstein Anomalisi diyagram\u0131<\/dd>\n<\/dl>\n<\/div>\n<p>Kalbimizi d\u00f6rt odac\u0131kl\u0131 bir ev gibi hayal edelim. Bu evin sa\u011f taraf\u0131ndaki iki oda, v\u00fccutta kullan\u0131lm\u0131\u015f, oksijeni azalm\u0131\u015f kan\u0131 toplay\u0131p temizlenmesi i\u00e7in akci\u011ferlere g\u00f6ndermekle g\u00f6revlidir. Sa\u011f \u00fcstteki oda (sa\u011f kulak\u00e7\u0131k) kan\u0131 toplar ve bu kan\u0131n, tek y\u00f6ne a\u00e7\u0131lan bir kap\u0131dan (trik\u00fcspit kapak) ge\u00e7erek sa\u011f alttaki pompa odas\u0131na (sa\u011f kar\u0131nc\u0131k) dolmas\u0131 gerekir. Bu kap\u0131n\u0131n g\u00f6revi, kan\u0131n sadece ileriye, yani pompa odas\u0131na ge\u00e7mesini sa\u011flamak ve geri ka\u00e7mas\u0131n\u0131 \u00f6nlemektir.<\/p>\n<p>\u0130\u015fte Ebstein anomalisinde temel sorun bu kap\u0131dad\u0131r. Trik\u00fcspit kapak, olmas\u0131 gereken do\u011fru yere de\u011fil daha a\u015fa\u011f\u0131ya, pompa odas\u0131n\u0131n (sa\u011f kar\u0131nc\u0131k) i\u00e7ine do\u011fru hatal\u0131 bir \u015fekilde monte edilmi\u015f gibidir. Dahas\u0131, kap\u0131y\u0131 olu\u015fturan yaprak\u00e7\u0131klar genellikle tam geli\u015fmemi\u015f, kal\u0131nla\u015fm\u0131\u015f ve esnekli\u011fini kaybetmi\u015ftir.<\/p>\n<p>Bu hatal\u0131 yerle\u015fim ve yap\u0131 y\u00fcz\u00fcnden kap\u0131 kapanamaz. Pompa odas\u0131 (sa\u011f kar\u0131nc\u0131k) kan\u0131 akci\u011ferlere g\u00f6ndermek i\u00e7in g\u00fc\u00e7l\u00fc bir \u015fekilde kas\u0131ld\u0131\u011f\u0131nda, kan\u0131n bir k\u0131sm\u0131 ileri gitmek yerine, tam kapanamayan bu kap\u0131dan geriye, kan\u0131n topland\u0131\u011f\u0131 sa\u011f kulak\u00e7\u0131\u011fa do\u011fru s\u0131zar. Biz bu duruma &#8220;trik\u00fcspit yetersizli\u011fi&#8221; veya &#8220;reg\u00fcrjitasyon&#8221; diyoruz.<\/p>\n<p>Bu durum kalbin \u00e7al\u0131\u015fma d\u00fczenini zamanla bozar. S\u00fcrekli geriye kan ka\u00e7t\u0131\u011f\u0131 i\u00e7in sa\u011f kulak\u00e7\u0131k geni\u015fler ve yorulur. Daha da \u00f6nemlisi, kapa\u011f\u0131n a\u015fa\u011f\u0131 kaymas\u0131yla, normalde g\u00fc\u00e7l\u00fc bir pompa olmas\u0131 gereken sa\u011f kar\u0131nc\u0131\u011f\u0131n bir k\u0131sm\u0131, i\u015flevini yitirir ve adeta sa\u011f kulak\u00e7\u0131\u011f\u0131n bir uzant\u0131s\u0131 gibi davranan ince duvarl\u0131, tembel bir keseye d\u00f6n\u00fc\u015f\u00fcr. Bu i\u015flevsiz b\u00f6l\u00fcme &#8220;atriyalize (kulak\u00e7\u0131kla\u015fm\u0131\u015f) sa\u011f ventrik\u00fcl&#8221; diyoruz. Bu b\u00f6l\u00fcm etkili bir kas\u0131lma yapamad\u0131\u011f\u0131 i\u00e7in, kalbin as\u0131l pompa g\u00fcc\u00fc azal\u0131r. Akci\u011ferlere kan\u0131 pompalayan etkili sa\u011f kar\u0131nc\u0131k k\u0131sm\u0131 ise normalden daha k\u00fc\u00e7\u00fck kal\u0131r ve \u00e7ok daha a\u011f\u0131r bir y\u00fck alt\u0131nda \u00e7al\u0131\u015fmak zorunda kal\u0131r.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_ile_birlikte_baska_kalp_sorunlari_gorulur_mu\"><\/span>Ebstein anomalisi ile birlikte ba\u015fka kalp sorunlar\u0131 g\u00f6r\u00fcl\u00fcr m\u00fc?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Evet, Ebstein anomalisi olan bireylerde s\u0131kl\u0131kla ba\u015fka kalp sorunlar\u0131 da tabloya e\u015flik eder. Bu durum tedaviyi planlarken g\u00f6z \u00f6n\u00fcnde bulundurdu\u011fumuz \u00f6nemli bir fakt\u00f6rd\u00fcr. En s\u0131k kar\u015f\u0131la\u015ft\u0131\u011f\u0131m\u0131z ek sorun, kalbin sa\u011f ve sol \u00fcst odac\u0131klar\u0131 (kulak\u00e7\u0131klar) aras\u0131ndaki duvarda bir delik olmas\u0131d\u0131r. Bu duruma e\u015flik edebilecek ba\u015fl\u0131ca sorunlar \u015funlard\u0131r:<\/p>\n<ul>\n<li aria-level=\"1\">Atriyal septal defekt (ASD)<\/li>\n<li aria-level=\"1\">Patent foramen ovale (PFO)<\/li>\n<li aria-level=\"1\">Kalp ritim bozukluklar\u0131 (aritmiler)<\/li>\n<li aria-level=\"1\">Wolff-Parkinson-White (WPW) sendromu<\/li>\n<li aria-level=\"1\">Pulmoner kapak darl\u0131\u011f\u0131 (pulmoner stenoz)<\/li>\n<li aria-level=\"1\">Pulmoner kapak yoklu\u011fu (pulmoner atrezi)<\/li>\n<\/ul>\n<p>Bu delikler (ASD veya PFO), oksijeni azalm\u0131\u015f kan\u0131n bir k\u0131sm\u0131n\u0131n, kalbin sol taraf\u0131ndaki temiz kanla kar\u0131\u015fmas\u0131na neden olabilir. Bu da v\u00fccuda daha az oksijenli kan gitmesine ve \u00f6zellikle bebeklerde ciltte morarmaya (siyanoz) yol a\u00e7ar. Kalp ritim bozukluklar\u0131 (aritmiler) ise Ebstein anomalisinde olduk\u00e7a yayg\u0131nd\u0131r ve \u00e7arp\u0131nt\u0131, ba\u015f d\u00f6nmesi gibi \u015fikayetlere neden olabilir. Wolff-Parkinson-White (WPW) sendromu, kalpte fazladan bir elektrik yolu bulunmas\u0131 durumudur ve ciddi ritim sorunlar\u0131n\u0131 tetikleyebilir. Bazen bu sorunlar\u0131n yan\u0131nda, nadir de olsa total pulmoner ven\u00f6z d\u00f6n\u00fc\u015f anomalisi gibi daha karma\u015f\u0131k tablolar da g\u00f6r\u00fclebilir. E\u015flik eden bu sorunlar\u0131n varl\u0131\u011f\u0131, \u00f6zellikle cerrahi planlamas\u0131 s\u0131ras\u0131nda b\u00fct\u00fcnc\u00fcl bir yakla\u015f\u0131mla ele al\u0131nmalar\u0131n\u0131 gerektirir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_neden_olur_ve_endiselenmeli_miyim\"><\/span>Ebstein anomalisi neden olur ve endi\u015felenmeli miyim?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Bu ebeveynlerin en \u00e7ok sordu\u011fu ve endi\u015felendi\u011fi sorulardan biridir. \u015eunu en ba\u015fta ve net bir \u015fekilde belirtmek gerekir: Ebstein anomalisinin kesin nedeni \u00e7o\u011fu vakada bilinmemektedir ve bu durum sizin veya e\u015finizin yapt\u0131\u011f\u0131 ya da yapmad\u0131\u011f\u0131 bir \u015feyden kaynaklanmaz. Bu hamileli\u011fin \u00e7ok erken d\u00f6nemlerinde, kalp geli\u015firken meydana gelen ve genellikle \u00f6nceden tahmin edilemeyen veya engellenemeyen bir olayd\u0131r.<\/p>\n<p>Ara\u015ft\u0131rmalar, genetik ve \u00e7evresel fakt\u00f6rlerin bir kombinasyonunun rol oynayabilece\u011fini d\u00fc\u015f\u00fcnd\u00fcrse de ortada net bir sebep-sonu\u00e7 ili\u015fkisi yoktur. Ailede ba\u015fka birinde do\u011fumsal kalp hastal\u0131\u011f\u0131 olmas\u0131 riski bir miktar art\u0131rabilir, ancak bu hastal\u0131\u011f\u0131n do\u011frudan ebeveynden \u00e7ocu\u011fa ge\u00e7ti\u011fi anlam\u0131na gelmez. Bu sadece genetik bir yatk\u0131nl\u0131\u011f\u0131n olabilece\u011fine i\u015faret eder.<\/p>\n<p>Ge\u00e7mi\u015fte baz\u0131 ila\u00e7lar\u0131n, \u00f6zellikle bipolar bozukluk tedavisinde kullan\u0131lan lityumun hamilelikte kullan\u0131m\u0131 ile Ebstein anomalisi aras\u0131nda zay\u0131f bir ba\u011flant\u0131 kurulmu\u015ftur. Ancak bu o kadar nadir bir durumdur ki bu ilac\u0131 kullanan annelerin ezici \u00e7o\u011funlu\u011funun bebekleri sa\u011fl\u0131kl\u0131 do\u011far. Bu t\u00fcr maddeler &#8220;do\u011frudan neden&#8221; de\u011fil sadece olas\u0131l\u0131\u011f\u0131 \u00e7ok k\u00fc\u00e7\u00fck bir oranda art\u0131rabilen &#8220;risk fakt\u00f6rleri&#8221; olarak kabul edilir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_ne_gibi_belirtilere_yol_acar\"><\/span>Ebstein anomalisi ne gibi belirtilere yol a\u00e7ar?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Ebstein anomalisinin belirtileri, hastal\u0131\u011f\u0131n \u015fiddetine ba\u011fl\u0131 olarak o kadar de\u011fi\u015fkendir ki baz\u0131 insanlar ileri yeti\u015fkinlik d\u00f6nemine kadar hi\u00e7bir \u015fey fark etmeyebilirken, baz\u0131 bebekler do\u011fumdan hemen sonra ciddi belirtiler g\u00f6sterebilir. Bu geni\u015f yelpaze, bazen tan\u0131n\u0131n neden gecikti\u011fini veya bir ki\u015finin neden &#8220;y\u0131llarca bir sorun ya\u015famad\u0131m da \u015fimdi ortaya \u00e7\u0131kt\u0131?&#8221; diye sordu\u011funu a\u00e7\u0131klar.<\/p>\n<p>Belirtiler genellikle ya\u015fa g\u00f6re farkl\u0131l\u0131k g\u00f6sterir. Yenido\u011fan ve bebeklik d\u00f6nemindeki ba\u015fl\u0131ca belirtiler \u015funlar olabilir:<\/p>\n<ul>\n<li aria-level=\"1\">Dudaklarda, dilde ve t\u0131rnaklarda morarma (siyanoz)<\/li>\n<li aria-level=\"1\">S\u0131k ve zorlu nefes alma<\/li>\n<li aria-level=\"1\">Beslenirken \u00e7abuk yorulma<\/li>\n<li aria-level=\"1\">Yeterli kilo alamama<\/li>\n<li aria-level=\"1\">V\u00fccutta, \u00f6zellikle bacaklarda \u015fi\u015flik<\/li>\n<li aria-level=\"1\">Doktor muayenesinde duyulan \u00fcf\u00fcr\u00fcm.<\/li>\n<\/ul>\n<p>Hastal\u0131\u011f\u0131n daha hafif formlar\u0131nda ise belirtiler \u00e7ocukluk veya yeti\u015fkinlik d\u00f6neminde ortaya \u00e7\u0131kabilir. Bu d\u00f6nemdeki s\u0131k g\u00f6r\u00fclen \u015fikayetler ise \u015f\u00f6yledir:<\/p>\n<ul>\n<li aria-level=\"1\">Eforla artan yorgunluk ve halsizlik<\/li>\n<li aria-level=\"1\">Merdiven \u00e7\u0131karken veya ko\u015farken nefes nefese kalma<\/li>\n<li aria-level=\"1\">Kalbin d\u00fczensiz, h\u0131zl\u0131 veya &#8220;tekleme&#8221; \u015feklinde atmas\u0131 (\u00e7arp\u0131nt\u0131)<\/li>\n<li aria-level=\"1\">Efor s\u0131ras\u0131nda beliren veya k\u00f6t\u00fcle\u015fen morarma<\/li>\n<li aria-level=\"1\">Bacaklarda veya kar\u0131nda \u015fi\u015flik (\u00f6dem)<\/li>\n<li aria-level=\"1\">Nadiren g\u00f6\u011f\u00fcs a\u011fr\u0131s\u0131<\/li>\n<li aria-level=\"1\">Nadiren ba\u015f d\u00f6nmesi veya bay\u0131lma.<\/li>\n<\/ul>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_tanisi_icin_hangi_testler_yapilir\"><\/span>Ebstein anomalisi tan\u0131s\u0131 i\u00e7in hangi testler yap\u0131l\u0131r?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Do\u011fru bir tan\u0131 koymak ve hastal\u0131\u011f\u0131n ciddiyetini net bir \u015fekilde anlamak, en uygun tedavi yolunu \u00e7izmemiz i\u00e7in hayati \u00f6nem ta\u015f\u0131r. Bu nedenle sadece tan\u0131y\u0131 do\u011frulamakla kalmay\u0131p, kalbinizin detayl\u0131 bir haritas\u0131n\u0131 \u00e7\u0131karmak i\u00e7in bir dizi testten faydalan\u0131r\u0131z. Bu s\u00fcre\u00e7te kullan\u0131lan ba\u015fl\u0131ca tan\u0131 y\u00f6ntemleri \u015funlard\u0131r.<\/p>\n<p>Ekokardiyografi (EKO): Bu test, Ebstein anomalisi tan\u0131s\u0131nda bizim alt\u0131n standard\u0131m\u0131zd\u0131r. Ses dalgalar\u0131 kullanan bir ultrason y\u00f6ntemidir. A\u011fr\u0131s\u0131zd\u0131r ve bize kalbinizin hareketli g\u00f6r\u00fcnt\u00fclerini verir. Bu sayede trik\u00fcspit kapa\u011f\u0131n nerede oldu\u011funu, yaprak\u00e7\u0131klar\u0131n\u0131n ne durumda oldu\u011funu ne kadar kan ka\u00e7\u0131rd\u0131\u011f\u0131n\u0131 ve kalp odac\u0131klar\u0131n\u0131n boyutlar\u0131n\u0131 net bir \u015fekilde g\u00f6r\u00fcr\u00fcz.<\/p>\n<p>Elektrokardiyogram (EKG): Kalbin elektriksel aktivitesini kaydeden bu basit test, ritim bozukluklar\u0131n\u0131 veya kalbin sa\u011f taraf\u0131ndaki b\u00fcy\u00fcmeye ba\u011fl\u0131 de\u011fi\u015fiklikleri saptamam\u0131za yard\u0131mc\u0131 olur.<\/p>\n<p>G\u00f6\u011f\u00fcs R\u00f6ntgeni: Bize kalbin genel boyutu ve \u015fekli hakk\u0131nda h\u0131zl\u0131 bir fikir verir. Genellikle Ebstein anomalisinde kalp g\u00f6lgesi normalden b\u00fcy\u00fck g\u00f6r\u00fcn\u00fcr.<\/p>\n<p>Kardiyak Manyetik Rezonans (Kardiyak MR): Bu ileri g\u00f6r\u00fcnt\u00fcleme tekni\u011fi, \u00f6zellikle sa\u011f kar\u0131nc\u0131\u011f\u0131n hacmi, kas yap\u0131s\u0131 ve fonksiyonlar\u0131 hakk\u0131nda EKO&#8217;dan bile daha detayl\u0131, \u00fc\u00e7 boyutlu bilgiler sa\u011flar. Cerrahi planlamas\u0131nda s\u0131k\u00e7a ba\u015fvurdu\u011fumuz bir y\u00f6ntemdir.<\/p>\n<p>Efor Testi: Bir ko\u015fu band\u0131nda veya bisiklette egzersiz yaparken kalbinizin nas\u0131l tepki verdi\u011fini, efor kapasitenizi ve egzersizle ortaya \u00e7\u0131kan bir ritim bozuklu\u011fu olup olmad\u0131\u011f\u0131n\u0131 de\u011ferlendiririz.<\/p>\n<p>Holter Monit\u00f6r\u00fc: Bu 24 veya 48 saat boyunca \u00fczerinizde ta\u015f\u0131d\u0131\u011f\u0131n\u0131z k\u00fc\u00e7\u00fck bir EKG cihaz\u0131d\u0131r. G\u00fcnl\u00fck ya\u015fam\u0131n\u0131z s\u0131ras\u0131nda ortaya \u00e7\u0131kan ancak k\u0131sa s\u00fcreli EKG&#8217;de yakalanamayan ritim bozukluklar\u0131n\u0131 tespit etmek i\u00e7in \u00e7ok de\u011ferlidir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_hangi_ciddi_sorunlara_komplikasyonlara_yol_acabilir\"><\/span>Ebstein anomalisi hangi ciddi sorunlara (komplikasyonlara) yol a\u00e7abilir?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Ebstein anomalisi, \u00f6zellikle ilerlemi\u015f vakalarda ve tedavi edilmedi\u011finde, kalbin \u00e7al\u0131\u015fma d\u00fczenini bozarak bir dizi ciddi soruna neden olabilir. Bu riskleri bilmek, d\u00fczenli takibin ve zaman\u0131nda m\u00fcdahalenin neden bu kadar \u00f6nemli oldu\u011funu anlamam\u0131za yard\u0131mc\u0131 olur. Olas\u0131 ba\u015fl\u0131ca komplikasyonlar \u015funlard\u0131r:<\/p>\n<ul>\n<li aria-level=\"1\">Kalp yetmezli\u011fi<\/li>\n<li aria-level=\"1\">Ritim bozukluklar\u0131 (aritmiler)<\/li>\n<li aria-level=\"1\">\u0130nme (paradoksal emboli)<\/li>\n<li aria-level=\"1\">Ani kardiyak \u00f6l\u00fcm<\/li>\n<li aria-level=\"1\">Siyanoz (morarma)<\/li>\n<li aria-level=\"1\">Egzersiz kapasitesinde d\u00fc\u015f\u00fc\u015f<\/li>\n<li aria-level=\"1\">Beyin apsesi (\u00e7ok nadir)<\/li>\n<li aria-level=\"1\">Kalp kapak iltihab\u0131 (enfektif endokardit)<\/li>\n<\/ul>\n<p>Bunlardan en s\u0131k g\u00f6r\u00fclenleri kalp yetmezli\u011fi ve ritim bozukluklar\u0131d\u0131r. Kalp yetmezli\u011fi, yorulan ve verimsiz \u00e7al\u0131\u015fan kalbin art\u0131k v\u00fccudun ihtiya\u00e7lar\u0131n\u0131 kar\u015f\u0131layamamas\u0131 durumudur. Ritim bozukluklar\u0131 ise \u00e7arp\u0131nt\u0131dan bay\u0131lmaya kadar giden \u015fikayetlere yol a\u00e7abilir ve kalp yetmezli\u011fini daha da k\u00f6t\u00fcle\u015ftirebilir. Kalpteki bir delikten (ASD) kaynaklanabilen inme riski ve kontrols\u00fcz aritmilere ba\u011fl\u0131 ani kardiyak \u00f6l\u00fcm riski ise nadir olmakla birlikte bu durumun ciddiye al\u0131nmas\u0131 gerekti\u011fini g\u00f6steren en \u00f6nemli komplikasyonlard\u0131r. D\u00fczenli takip ve modern tedavi y\u00f6ntemleriyle bu riskler y\u00f6netilebilir ve \u00f6nemli \u00f6l\u00e7\u00fcde azalt\u0131labilir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_icin_ameliyatsiz_tedavi_secenekleri_var_midir\"><\/span>Ebstein anomalisi i\u00e7in ameliyats\u0131z tedavi se\u00e7enekleri var m\u0131d\u0131r?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Evet, \u00f6zellikle belirtisi olmayan veya \u00e7ok hafif \u015fikayetleri olan hastalar i\u00e7in ameliyats\u0131z tedavi y\u00f6ntemleri mevcuttur. Bu tedavilerin amac\u0131 hastal\u0131\u011f\u0131 &#8220;yok etmek&#8221; de\u011fil belirtileri y\u00f6netmek, kalbin i\u015f y\u00fck\u00fcn\u00fc azaltmak ve ciddi komplikasyonlar\u0131 \u00f6nlemektir.<\/p>\n<p>D\u00fczenli G\u00f6zlem ve Takip: Bu en s\u0131k ba\u015fvurdu\u011fumuz yakla\u015f\u0131md\u0131r. Ancak bu pasif bir &#8220;bekle ve g\u00f6r&#8221; s\u00fcreci de\u011fildir. Aksine, d\u00fczenli kontrollerle (genellikle y\u0131lda bir kez EKO ve EKG ile) kalbin durumunu aktif olarak izledi\u011fimiz, olas\u0131 bir k\u00f6t\u00fcle\u015fmeyi \u00e7ok erken bir evrede saptayarak cerrahi gibi daha ileri tedaviler i\u00e7in en do\u011fru zaman\u0131 belirlemeye \u00e7al\u0131\u015ft\u0131\u011f\u0131m\u0131z proaktif bir s\u00fcre\u00e7tir.<\/p>\n<p>\u0130la\u00e7 Tedavisi: Belirtileri kontrol etmek ve komplikasyonlar\u0131 tedavi etmek i\u00e7in \u00e7e\u015fitli ila\u00e7 gruplar\u0131ndan faydalan\u0131r\u0131z. Ba\u015fl\u0131ca kulland\u0131\u011f\u0131m\u0131z ila\u00e7 gruplar\u0131 \u015funlard\u0131r:<\/p>\n<ul>\n<li aria-level=\"1\">Di\u00fcretikler (idrar s\u00f6kt\u00fcr\u00fcc\u00fcler)<\/li>\n<li aria-level=\"1\">Anti-aritmik ila\u00e7lar<\/li>\n<li aria-level=\"1\">Antikoag\u00fclanlar (kan suland\u0131r\u0131c\u0131lar)<\/li>\n<li aria-level=\"1\">Beta blokerler<\/li>\n<li aria-level=\"1\">Digoksin<\/li>\n<\/ul>\n<p>Bu ila\u00e7lar, kalp yetmezli\u011fi belirtilerini hafifletmek, ritim bozukluklar\u0131n\u0131 kontrol alt\u0131nda tutmak veya inme riskini azaltmak gibi hedeflere y\u00f6nelik olarak ki\u015fiye \u00f6zel bir \u015fekilde re\u00e7ete edilir.<\/p>\n<p>Kateter Ablasyonu: Bu ameliyats\u0131z bir ritim bozuklu\u011fu tedavi y\u00f6ntemidir. \u00d6zellikle ila\u00e7lara yan\u0131t vermeyen veya WPW sendromu gibi altta yatan belirli bir elektrik yoluna ba\u011fl\u0131 ritim bozukluklar\u0131 olan hastalarda kullan\u0131l\u0131r. Kas\u0131ktan ince bir telle (kateter) kalbe girilerek ritim bozuklu\u011funa neden olan anormal odak bulunur ve \u0131s\u0131 veya dondurma enerjisiyle etkisiz hale getirilir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_ameliyati_ne_zaman_ve_kimler_icin_gereklidir\"><\/span>Ebstein anomalisi ameliyat\u0131 ne zaman ve kimler i\u00e7in gereklidir?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Ameliyat karar\u0131, hayat kalitesini d\u00fc\u015f\u00fcren belirtiler kalbin giderek b\u00fcy\u00fcmesi veya fonksiyonlar\u0131n\u0131n bozulmas\u0131 gibi objektif bulgular ortaya \u00e7\u0131kt\u0131\u011f\u0131nda verilir. Bu karar, her hasta i\u00e7in ayr\u0131 ayr\u0131, pek \u00e7ok fakt\u00f6r g\u00f6z \u00f6n\u00fcnde bulundurularak al\u0131n\u0131r. Ameliyat i\u00e7in en do\u011fru zaman\u0131 belirlemek, tedavinin ba\u015far\u0131s\u0131ndaki en kritik ad\u0131mlardan biridir. Ameliyat gerektiren ba\u015fl\u0131ca durumlar \u015funlard\u0131r:<\/p>\n<ul>\n<li aria-level=\"1\">G\u00fcnl\u00fck ya\u015fam\u0131 k\u0131s\u0131tlayan ve ila\u00e7la kontrol edilemeyen belirtiler (nefes darl\u0131\u011f\u0131, yorgunluk)<\/li>\n<li aria-level=\"1\">\u0130lerleyici kalp yetmezli\u011fi bulgular\u0131<\/li>\n<li aria-level=\"1\">Efor testlerinde saptanan, egzersiz kapasitesinde ilerleyici d\u00fc\u015f\u00fc\u015f<\/li>\n<li aria-level=\"1\">EKO veya MR&#8217;da g\u00f6r\u00fclen, kalp boyutlar\u0131nda (\u00f6zellikle sa\u011f kalp) s\u00fcrekli art\u0131\u015f<\/li>\n<li aria-level=\"1\">\u0130stirahat veya hafif eforla ortaya \u00e7\u0131kan morarma (siyanoz)<\/li>\n<li aria-level=\"1\">Daha \u00f6nce inme veya beyne p\u0131ht\u0131 atmas\u0131 \u00f6yk\u00fcs\u00fc<\/li>\n<li aria-level=\"1\">\u0130la\u00e7 veya ablasyona yan\u0131t vermeyen, hayat\u0131 tehdit eden ritim bozukluklar\u0131<\/li>\n<\/ul>\n<p>Bazen, hen\u00fcz ciddi belirtileri olmasa da testlerde kalbinde &#8220;sessiz bir ilerleme&#8221; saptanan hastalara, kalpte geri d\u00f6n\u00fc\u015f\u00fcms\u00fcz hasar olu\u015fmadan \u00f6nce proaktif olarak ameliyat \u00f6nerebiliriz. \u00d6zellikle \u00e7ocuklarda, kalbin daha fazla bozulmas\u0131n\u0131 \u00f6nlemek amac\u0131yla erken ya\u015flarda yap\u0131lacak ba\u015far\u0131l\u0131 bir tamir, uzun d\u00f6nem sonu\u00e7lar\u0131 \u00e7ok daha iyi hale getirebilir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_cerrahisinde_hangi_ameliyat_yontemleri_uygulanir\"><\/span>Ebstein anomalisi cerrahisinde hangi ameliyat y\u00f6ntemleri uygulan\u0131r?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Ebstein anomalisi cerrahisinde amac\u0131m\u0131z, \u00f6ncelikli olarak hastan\u0131n kendi kapak dokusunu koruyarak, anormal yap\u0131y\u0131 m\u00fcmk\u00fcn olan en normal ve i\u015flevsel hale getirmektir. Bu felsefeyle geli\u015ftirilen ve g\u00fcn\u00fcm\u00fczde &#8220;alt\u0131n standart&#8221; olarak kabul edilen y\u00f6ntem Kon (Cone) Prosed\u00fcr\u00fc&#8217;d\u00fcr.<\/p>\n<p>Kon (Cone) Prosed\u00fcr\u00fc: Bu Ebstein anomalisinin karma\u015f\u0131k anatomisini \u00fc\u00e7 boyutlu olarak d\u00fczelten, son derece ustal\u0131k gerektiren bir tamir tekni\u011fidir. Ameliyat s\u0131ras\u0131nda, yerinden kaym\u0131\u015f ve yap\u0131\u015fm\u0131\u015f olan kapak yaprak\u00e7\u0131klar\u0131, bir heykelt\u0131ra\u015f\u0131n titizli\u011fiyle kalp kas\u0131ndan serbestle\u015ftirilir. Daha sonra bu serbestle\u015fen kapak dokular\u0131, olmas\u0131 gereken do\u011fru anatomik seviyeye \u00e7ekilir ve bir &#8220;k\u00fclah&#8221; veya &#8220;huni&#8221; (\u0130ngilizce: cone) olu\u015fturacak \u015fekilde yeniden bir araya getirilerek dikilir. Bu sayede hastan\u0131n tamamen kendi dokusundan, s\u0131z\u0131nt\u0131 yapmayan, fonksiyonel yeni bir kapak olu\u015fturulur. Kon prosed\u00fcr\u00fcn\u00fcn en b\u00fcy\u00fck avantaj\u0131, protez kapak kullan\u0131m\u0131n\u0131 ortadan kald\u0131rmas\u0131 ve \u00f6zellikle \u00e7ocuklarda tamir edilen kapa\u011f\u0131n \u00e7ocukla birlikte b\u00fcy\u00fcme potansiyeline sahip olmas\u0131d\u0131r. Bu gelecekte tekrar ameliyat olma ihtiyac\u0131n\u0131 \u00f6nemli \u00f6l\u00e7\u00fcde azalt\u0131r.<\/p>\n<p>Trik\u00fcspit Kapak De\u011fi\u015fimi: E\u011fer hastan\u0131n kendi kapak dokusu, ileri derecede hasarl\u0131 oldu\u011fu i\u00e7in tamire uygun de\u011filse veya daha \u00f6nceki tamir denemeleri ba\u015far\u0131s\u0131z olduysa, kapak de\u011fi\u015fimi bir se\u00e7enektir. Bu durumda hastal\u0131kl\u0131 kapak \u00e7\u0131kar\u0131l\u0131r ve yerine bir protez kapak (biyolojik veya mekanik) tak\u0131l\u0131r. Ancak bu y\u00f6ntem protez kapaklar\u0131n zamanla y\u0131pranmas\u0131 veya \u00f6m\u00fcr boyu kan suland\u0131r\u0131c\u0131 ila\u00e7 gerektirmesi gibi potansiyel dezavantajlar\u0131 nedeniyle, tamirin m\u00fcmk\u00fcn olmad\u0131\u011f\u0131 durumlarla s\u0131n\u0131rland\u0131r\u0131lmal\u0131d\u0131r. Kon prosed\u00fcr\u00fcn\u00fcn yayg\u0131nla\u015fmas\u0131yla kapak de\u011fi\u015fimi ihtiyac\u0131 \u00f6nemli \u00f6l\u00e7\u00fcde azalm\u0131\u015ft\u0131r.<\/p>\n<p>Ameliyat s\u0131ras\u0131nda, e\u011fer varsa kulak\u00e7\u0131klar aras\u0131 delik (ASD) de mutlaka kapat\u0131l\u0131r ve gerekli g\u00f6r\u00fclen hastalarda ritim bozukluklar\u0131na y\u00f6nelik cerrahi ablasyon (Maze prosed\u00fcr\u00fc) gibi ek i\u015flemler de ayn\u0131 seansta yap\u0131larak, tek bir ameliyatla t\u00fcm sorunlar\u0131n \u00e7\u00f6z\u00fclmesi hedeflenir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_ameliyati_sonrasi_surec_ve_uzun_donem_takip_nasil_isler\"><\/span>Ebstein anomalisi ameliyat\u0131 sonras\u0131 s\u00fcre\u00e7 ve uzun d\u00f6nem takip nas\u0131l i\u015fler?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Ba\u015far\u0131l\u0131 bir ameliyat sonras\u0131, hastalar\u0131n ya\u015fam kalitesinde genellikle \u00e7arp\u0131c\u0131 bir iyile\u015fme g\u00f6r\u00fcl\u00fcr. Ancak bu tedavinin bitti\u011fi anlam\u0131na gelmez. Aksine, \u00f6m\u00fcr boyu s\u00fcrecek d\u00fczenli bir takibin ba\u015flang\u0131c\u0131d\u0131r.<\/p>\n<p>Ameliyat sonras\u0131 iyile\u015fme d\u00f6neminde dikkat edilmesi gereken baz\u0131 noktalar vard\u0131r:<\/p>\n<ul>\n<li aria-level=\"1\">A\u011fr\u0131 kontrol\u00fc<\/li>\n<li aria-level=\"1\">Yara bak\u0131m\u0131<\/li>\n<li aria-level=\"1\">Kademeli olarak aktiviteye d\u00f6n\u00fc\u015f<\/li>\n<li aria-level=\"1\">A\u011f\u0131r kald\u0131rmaktan ka\u00e7\u0131nma (ilk 6-8 hafta)<\/li>\n<li aria-level=\"1\">\u0130la\u00e7lar\u0131n d\u00fczenli kullan\u0131m\u0131<\/li>\n<\/ul>\n<p>Hastaneden taburcu olduktan sonraki hayat\u0131n\u0131zda ise, do\u011fumsal kalp hastal\u0131klar\u0131 konusunda uzmanla\u015fm\u0131\u015f bir kardiyolog taraf\u0131ndan \u00f6m\u00fcr boyu takip edilmeniz \u015fartt\u0131r. Bu takipler, genellikle y\u0131lda bir kez yap\u0131l\u0131r ve \u015fu ama\u00e7lar\u0131 g\u00fcder:<\/p>\n<ul>\n<li aria-level=\"1\">Ameliyat edilen kapa\u011f\u0131n fonksiyonunu de\u011ferlendirmek<\/li>\n<li aria-level=\"1\">Kalp boyutlar\u0131n\u0131 ve fonksiyonlar\u0131n\u0131 izlemek<\/li>\n<li aria-level=\"1\">Yeni ritim bozukluklar\u0131 geli\u015fip geli\u015fmedi\u011fini kontrol etmek<\/li>\n<li aria-level=\"1\">Genel sa\u011fl\u0131k durumunuzu ve ya\u015fam kalitenizi korumak<\/li>\n<\/ul>\n<p>Bu d\u00fczenli takipler, olas\u0131 sorunlar\u0131 \u00e7ok erken bir evrede saptamam\u0131z\u0131 ve proaktif bir \u015fekilde m\u00fcdahale etmemizi sa\u011flar. Bu uzun ve sa\u011fl\u0131kl\u0131 bir ya\u015fam s\u00fcrmenin en \u00f6nemli g\u00fcvencesidir.<\/p>\n<h2><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_ile_saglikli_bir_yasam_surmek_mumkun_mu\"><\/span>Ebstein anomalisi ile sa\u011fl\u0131kl\u0131 bir ya\u015fam s\u00fcrmek m\u00fcmk\u00fcn m\u00fc?<span class=\"ez-toc-section-end\"><\/span><\/h2>\n<p>Kesinlikle evet. Bu sorunun cevab\u0131, son y\u0131llardaki t\u0131bbi ve cerrahi geli\u015fmeler sayesinde her zamankinden daha olumludur. Ebstein anomalisi ciddi ve \u00f6m\u00fcr boyu takip gerektiren bir durum olsa da hastalar\u0131n b\u00fcy\u00fck bir \u00e7o\u011funlu\u011fu, do\u011fru zamanda yap\u0131lan do\u011fru tedavilerle aktif, \u00fcretken ve mutlu bir ya\u015fam s\u00fcrebilir.<\/p>\n<p>Hastal\u0131\u011f\u0131n hafif formlar\u0131 olan baz\u0131 ki\u015filer neredeyse hi\u00e7 k\u0131s\u0131tlama olmadan ya\u015fayabilirler. Ciddi vakalarda ise, \u00f6zellikle Kon prosed\u00fcr\u00fc gibi ba\u015far\u0131l\u0131 bir ameliyat sonras\u0131, hastalar spora d\u00f6nebilir, okula veya i\u015fe gidebilir, evlenebilir ve aile kurabilirler.<\/p>\n<p>Burada kilit nokta, durumuyla bar\u0131\u015f\u0131k, bilin\u00e7li bir ya\u015fam tarz\u0131 benimsemektir. Bu \u015fu anlama gelir:<\/p>\n<ul>\n<li aria-level=\"1\">Doktor kontrollerini asla aksatmamak<\/li>\n<li aria-level=\"1\">\u0130la\u00e7lar\u0131 d\u00fczenli kullanmak<\/li>\n<li aria-level=\"1\">Egzersiz program\u0131n\u0131 mutlaka doktora dan\u0131\u015farak belirlemek<\/li>\n<li aria-level=\"1\">Kalp sa\u011fl\u0131\u011f\u0131na uygun beslenmek (tuzu azaltmak gibi)<\/li>\n<li aria-level=\"1\">Gebelik gibi \u00f6nemli ya\u015fam kararlar\u0131n\u0131 mutlaka kardiyolog ve ilgili di\u011fer uzmanlarla planlayarak almak<\/li>\n<li aria-level=\"1\">V\u00fccudunuzdan gelen sinyallere (yorgunluk, \u00e7arp\u0131nt\u0131 gibi) kar\u015f\u0131 duyarl\u0131 olmak<\/li>\n<\/ul>\n<p>Ebstein anomalisi ile ya\u015fam bir yolculuktur ve bu yolculukta, uzman hekimlerden olu\u015fan ekibiniz her zaman sizin yan\u0131n\u0131zda olacakt\u0131r. Modern t\u0131p, bu nadir durumda bile hastalar\u0131n uzun ve kaliteli bir ya\u015fam s\u00fcrmesi i\u00e7in g\u00fc\u00e7l\u00fc olanaklar sunmaktad\u0131r.<br \/>\n<h2 class=\"accordion_title\"><span class=\"ez-toc-section\" id=\"Sikca_Sorulan_Sorular\"><\/span>S\u0131k\u00e7a Sorulan Sorular<span class=\"ez-toc-section-end\"><\/span><\/h2><div class=\"accordion\">\n\t<div id=\"accordion-2045154811\" class=\"accordion-item\">\n\t\t<a id=\"accordion-2045154811-label\" class=\"accordion-title plain\" href=\"#accordion-item-ebstein-anomalisi-nedir?\" aria-expanded=\"false\" aria-controls=\"accordion-2045154811-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_nedir\"><\/span>Ebstein anomalisi nedir?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-2045154811-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-2045154811-label\" >\n\t\t\t\n<p>Do\u011fu\u015ftan gelen nadir bir kalp hastal\u0131\u011f\u0131d\u0131r. Trik\u00fcspit kapak normalden daha a\u015fa\u011f\u0131da yer al\u0131r ve kalbin sa\u011f taraf\u0131nda yap\u0131sal bozukluklara neden olur.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-702067284\" class=\"accordion-item\">\n\t\t<a id=\"accordion-702067284-label\" class=\"accordion-title plain\" href=\"#accordion-item-bu-hastal\u0131k-ne-zaman-ortaya-\u00e7\u0131kar?\" aria-expanded=\"false\" aria-controls=\"accordion-702067284-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Bu_hastalik_ne_zaman_ortaya_cikar\"><\/span>Bu hastal\u0131k ne zaman ortaya \u00e7\u0131kar?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-702067284-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-702067284-label\" >\n\t\t\t\n<p>Do\u011fumla birlikte mevcuttur; baz\u0131 vakalar do\u011fumda fark edilirken baz\u0131lar\u0131 ileri ya\u015flarda belirti verir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-602505541\" class=\"accordion-item\">\n\t\t<a id=\"accordion-602505541-label\" class=\"accordion-title plain\" href=\"#accordion-item-ebstein-anomalisi-belirtileri-nelerdir?\" aria-expanded=\"false\" aria-controls=\"accordion-602505541-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_belirtileri_nelerdir\"><\/span>Ebstein anomalisi belirtileri nelerdir?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-602505541-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-602505541-label\" >\n\t\t\t\n<p>Morarma (siyanoz), \u00e7abuk yorulma, nefes darl\u0131\u011f\u0131, \u00e7arp\u0131nt\u0131, bay\u0131lma ve geli\u015fim gerili\u011fi g\u00f6r\u00fclebilir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-151280419\" class=\"accordion-item\">\n\t\t<a id=\"accordion-151280419-label\" class=\"accordion-title plain\" href=\"#accordion-item-hangi-kapak-etkilenir?\" aria-expanded=\"false\" aria-controls=\"accordion-151280419-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Hangi_kapak_etkilenir\"><\/span>Hangi kapak etkilenir?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-151280419-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-151280419-label\" >\n\t\t\t\n<p>Sa\u011f kulak\u00e7\u0131k ile sa\u011f kar\u0131nc\u0131k aras\u0131ndaki trik\u00fcspit kapak etkilenir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-2389229144\" class=\"accordion-item\">\n\t\t<a id=\"accordion-2389229144-label\" class=\"accordion-title plain\" href=\"#accordion-item-bu-hastal\u0131k-neden-olur?\" aria-expanded=\"false\" aria-controls=\"accordion-2389229144-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Bu_hastalik_neden_olur\"><\/span>Bu hastal\u0131k neden olur?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-2389229144-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-2389229144-label\" >\n\t\t\t\n<p>Kesin nedeni bilinmez; ancak genetik fakt\u00f6rler ve baz\u0131 gebelik d\u00f6nemi etkiler rol oynayabilir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-767501296\" class=\"accordion-item\">\n\t\t<a id=\"accordion-767501296-label\" class=\"accordion-title plain\" href=\"#accordion-item-nas\u0131l-te\u015fhis-edilir?\" aria-expanded=\"false\" aria-controls=\"accordion-767501296-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Nasil_teshis_edilir\"><\/span>Nas\u0131l te\u015fhis edilir?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-767501296-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-767501296-label\" >\n\t\t\t\n<p>Ekokardiyografi (EKO), elektrokardiyografi (EKG), g\u00f6\u011f\u00fcs r\u00f6ntgeni ve baz\u0131 durumlarda kardiyak MR ile te\u015fhis edilir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-3152213388\" class=\"accordion-item\">\n\t\t<a id=\"accordion-3152213388-label\" class=\"accordion-title plain\" href=\"#accordion-item-ebstein-anomalisi-her-zaman-belirti-verir-mi?\" aria-expanded=\"false\" aria-controls=\"accordion-3152213388-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Ebstein_anomalisi_her_zaman_belirti_verir_mi\"><\/span>Ebstein anomalisi her zaman belirti verir mi?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-3152213388-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-3152213388-label\" >\n\t\t\t\n<p>Hay\u0131r, hafif formlar\u0131 belirti vermeyebilir ve tesad\u00fcfen saptanabilir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-2115152712\" class=\"accordion-item\">\n\t\t<a id=\"accordion-2115152712-label\" class=\"accordion-title plain\" href=\"#accordion-item-hastal\u0131\u011f\u0131n-ciddiyeti-ki\u015fiden-ki\u015fiye-de\u011fi\u015fir-mi?\" aria-expanded=\"false\" aria-controls=\"accordion-2115152712-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Hastaligin_ciddiyeti_kisiden_kisiye_degisir_mi\"><\/span>Hastal\u0131\u011f\u0131n ciddiyeti ki\u015fiden ki\u015fiye de\u011fi\u015fir mi?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-2115152712-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-2115152712-label\" >\n\t\t\t\n<p>Evet, trik\u00fcspit kapa\u011f\u0131n yerle\u015fim \u015fekline ve sa\u011f kalp fonksiyonuna g\u00f6re hafif ila a\u011f\u0131r aras\u0131nda de\u011fi\u015febilir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-4078865447\" class=\"accordion-item\">\n\t\t<a id=\"accordion-4078865447-label\" class=\"accordion-title plain\" href=\"#accordion-item-cerrahi-tedavi-gerekir-mi?\" aria-expanded=\"false\" aria-controls=\"accordion-4078865447-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Cerrahi_tedavi_gerekir_mi\"><\/span>Cerrahi tedavi gerekir mi?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-4078865447-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-4078865447-label\" >\n\t\t\t\n<p>A\u011f\u0131r semptomlar\u0131 olan hastalarda trik\u00fcspit kapak tamiri veya de\u011fi\u015fimi gibi cerrahi tedaviler gerekebilir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-2312326384\" class=\"accordion-item\">\n\t\t<a id=\"accordion-2312326384-label\" class=\"accordion-title plain\" href=\"#accordion-item-kateterle-tedavi-m\u00fcmk\u00fcn-m\u00fc?\" aria-expanded=\"false\" aria-controls=\"accordion-2312326384-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Kateterle_tedavi_mumkun_mu\"><\/span>Kateterle tedavi m\u00fcmk\u00fcn m\u00fc?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-2312326384-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-2312326384-label\" >\n\t\t\t\n<p>Baz\u0131 ritim bozukluklar\u0131nda kateter ablasyon tedavisi uygulanabilir; ancak kapak d\u00fczeltmesi i\u00e7in cerrahi gerekir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-4191603627\" class=\"accordion-item\">\n\t\t<a id=\"accordion-4191603627-label\" class=\"accordion-title plain\" href=\"#accordion-item-bu-hastal\u0131k-kalp-ritmini-etkiler-mi?\" aria-expanded=\"false\" aria-controls=\"accordion-4191603627-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Bu_hastalik_kalp_ritmini_etkiler_mi\"><\/span>Bu hastal\u0131k kalp ritmini etkiler mi?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-4191603627-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-4191603627-label\" >\n\t\t\t\n<p>Evet, kalpte ritim bozukluklar\u0131 s\u0131k g\u00f6r\u00fcl\u00fcr. \u00d6zellikle Wolff-Parkinson-White (WPW) sendromu e\u015flik edebilir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-1165652221\" class=\"accordion-item\">\n\t\t<a id=\"accordion-1165652221-label\" class=\"accordion-title plain\" href=\"#accordion-item-hamilelikte-ebstein-anomalisi-riskli-midir?\" aria-expanded=\"false\" aria-controls=\"accordion-1165652221-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Hamilelikte_Ebstein_anomalisi_riskli_midir\"><\/span>Hamilelikte Ebstein anomalisi riskli midir?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-1165652221-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-1165652221-label\" >\n\t\t\t\n<p>Evet, hamilelik s\u00fcreci dikkatli izlenmelidir; kalp yetersizli\u011fi riski artabilir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-4013531335\" class=\"accordion-item\">\n\t\t<a id=\"accordion-4013531335-label\" class=\"accordion-title plain\" href=\"#accordion-item-ya\u015fam-beklentisi-nas\u0131ld\u0131r?\" aria-expanded=\"false\" aria-controls=\"accordion-4013531335-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Yasam_beklentisi_nasildir\"><\/span>Ya\u015fam beklentisi nas\u0131ld\u0131r?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-4013531335-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-4013531335-label\" >\n\t\t\t\n<p>Erken te\u015fhis ve uygun tedavi ile ya\u015fam beklentisi olduk\u00e7a iyidir. Hafif formlar ya\u015fam\u0131 fazla etkilemez.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n\t<div id=\"accordion-3323976674\" class=\"accordion-item\">\n\t\t<a id=\"accordion-3323976674-label\" class=\"accordion-title plain\" href=\"#accordion-item-egzersiz-yap\u0131labilir-mi?\" aria-expanded=\"false\" aria-controls=\"accordion-3323976674-content\" >\n\t\t\t<button class=\"toggle\" aria-label=\"Toggle\"><i class=\"icon-angle-down\"><\/i><\/button>\n\t\t\t<h3 class=\"accordion-heading\" role=\"heading\" aria-level=\"3\"><span class=\"ez-toc-section\" id=\"Egzersiz_yapilabilir_mi\"><\/span>Egzersiz yap\u0131labilir mi?<span class=\"ez-toc-section-end\"><\/span><\/h3>\n\t\t<\/a>\n\t\t<div id=\"accordion-3323976674-content\" class=\"accordion-inner\" aria-labelledby=\"accordion-3323976674-label\" >\n\t\t\t\n<p>Hafif formlarda uygun d\u00fczeyde egzersiz m\u00fcmk\u00fcnd\u00fcr. Ciddi vakalarda doktor \u00f6nerisine g\u00f6re hareket edilmelidir.<\/p>\n\t\t<\/div>\n\t<\/div>\n\t\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>Ebstein anomalisi, trik\u00fcspit kapa\u011f\u0131n do\u011fu\u015ftan yap\u0131sal bozuklu\u011fu ile karakterize nadir bir kalp hastal\u0131\u011f\u0131d\u0131r. Bu durumda trik\u00fcspit kapak yaprak\u00e7\u0131klar\u0131 normalden a\u015fa\u011f\u0131da, sa\u011f kar\u0131nc\u0131\u011fa do\u011fru yerle\u015fmi\u015ftir ve kapak tam olarak kapanamaz. Kapa\u011f\u0131n anormal konumu nedeniyle sa\u011f kulak\u00e7\u0131k geni\u015fler, sa\u011f kar\u0131nc\u0131k k\u00fc\u00e7\u00fcl\u00fcr ve kan\u0131n geriye ka\u00e7\u0131\u015f\u0131 (trik\u00fcspit yetmezli\u011fi) olu\u015fur. Bu durum, kalbin pompalama verimini d\u00fc\u015f\u00fcr\u00fcr ve zamanla sa\u011f [&#8230;]\n","protected":false},"author":7,"featured_media":9031,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[234],"tags":[419],"class_list":["post-11119","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-uncategorized","tag-ebstein-anomalisi-nedir-en"],"_links":{"self":[{"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/posts\/11119","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/users\/7"}],"replies":[{"embeddable":true,"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/comments?post=11119"}],"version-history":[{"count":3,"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/posts\/11119\/revisions"}],"predecessor-version":[{"id":13299,"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/posts\/11119\/revisions\/13299"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/media\/9031"}],"wp:attachment":[{"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/media?parent=11119"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/categories?post=11119"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/dryavuzbesogul.com\/en\/wp-json\/wp\/v2\/tags?post=11119"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}